epilepsiaEpilepsy and paroxysmal conditionsЭпилепсия и пароксизмальные состояния2077-83332311-4088IRBIS LLCepilepsia-179Research ArticleORIGINAL ARTICLESОРИГИНАЛЬНЫЕ СТАТЬИBENIGN OCCIPITAL EPILEPSY OF CHILDHOOD: FACTORS AFFECTING THE PARTICULARS OF TREATMENTДОБРОКАЧЕСТВЕННАЯ ЗАТЫЛОЧНАЯ ЭПИЛЕПСИЯ У ДЕТЕЙ: ФАКТОРЫ, ВЛИЯЮЩИЕ НА ОСОБЕННОСТИ ТЕЧЕНИЯЩедеркинаИ. О.ShederkinaI. O.

Детская консультативная неврологическая поликлиника при Морозовской ДГКБ

Children’s consulting neurologic outpatient clinic at Morozov children’s city clinical hospital

КарловВ. А.KarlovV. A.

Детская консультативная неврологическая поликлиника при Морозовской ДГКБ

Children’s consulting neurologic outpatient clinic at Morozov children’s city clinical hospital

МГМСУРоссияMGMSURussian Federation201021082016213746Copyright © Shederkina I.O., Karlov V.A., 20162016Щедеркина И.О., Карлов В.А.Shederkina I.O., Karlov V.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.epilepsia.su/jour/article/view/179

Two forms of occipital epilepsy of childhood are distinguished which are known as Panayiotopoulos syndrome (PS) and Gastaut syndrome (GS). This article reviews modern literature data on epidemiology, diagnosis, electro-clinical characteristics, differential diagnosis and treatment principles of both syndromes. Also, the results of observation of 17 children with PS aged from 4 to 13 years, for a period from 9 months to 8 years, are given. In the course of assessment of clinical encephalographic particular features of PS, the number of seizures recorded during the observation period was taken as a criterion of “severity” of disease course, namely: group A – less than 5 seizures, (5 children), and group B – over 5 seizures (12 children). Also, 30 children with established GS diagnosis aged from 3 to 14 years, and remained under observation for 1-8 years, were examined. Patients were divided in three groups based on the number of simple, complex partial seizures and secondary generalized tonic-clonic seizures before the beginning of anticonvulsant therapy. In the course of study the factors have been revealed that affect the frequency and severity of seizures, which defined the duration and intensity of treatment, as well as the prognosis of disease.

выделяют две формы детской затылочной эпилепсии, которые известны как синдром Panayiotopoulos (СП) и синдром Gastaut (СГ). В статье приведены данные современной литературы по эпидемиологии, диагностике, электроклинической характеристике, дифференциальной диагностике и принципах терапии обоих синдромов. Также приведены результаты наблюдения 17 детей с СП в возрасте от 4 до 13 лет: время наблюдения составило от 9 мес до 8 лет. В процессе оценки клинико-энцефалографических особенностей СП за критерий «тяжести» течения было взято количество приступов, зарегистрированных за время наблюдения (группа А – менее 5 приступов, 5 детей; группа В – более 5 приступов, 12 детей). Было обследовано и 30 детей с установленным диагнозом СГ в возрасте от 3 до 14 лет, находящихся под наблюдением в течение 1-8 лет. Пациенты были разделены на три группы по количеству простых, сложных парциальных приступов и вторично- генерализованных тонико-клонических приступов до начала противосудорожной терапии. В ходе исследования были выявлены факторы, влияющие на частоту и тяжесть приступов, что определило длительность и интенсивность терапии, а также прогноз заболевания.

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The authors declare that there are no conflicts of interest present.