epilepsiaEpilepsy and paroxysmal conditionsЭпилепсия и пароксизмальные состояния2077-83332311-4088IRBIS LLC10.17749/2077-8333/epi.par.con.2022.123epilepsia-792Research ArticleEDITORIAL ARTICLESРЕДАКЦИОННАЯ СТАТЬЯEpilepsy syndromes: the 2022 ILAE definition and classificationЭпилептические синдромы: определение и классификация Международной Противоэпилептической Лиги 2022 годаhttps://orcid.org/0000-0002-7663-710XБлиновД. В.BlinovD. V.

Блинов Дмитрий Владиславович – к.м.н., руководитель по научным и медицинским вопросам; врач-невролог

WoS ResearcherID: J-4946-2017;

Scopus Author ID: 7003589812;

РИНЦ SPIN-код: 6317-9833

ул. Садовая-Триумфальная, д. 4/10, Москва 127006

1-е Успенское ш., д. 111, Московская обл., Одинцовский р-н, Лапино 143081

 

Dmitry V. Blinov – MD, PhD, MBA, Head of Medical and Scientific Affairs; Neurologist

WoS ResearcherID: J-4946-2017;

Scopus Author ID: 7003589812;

RSCI SPIN-code: 6317-98334/10

Sadovaya-Triumfalnaya Str., Moscow 127006

111 1st Uspenskoye Hwy, Moscow Region, Odintsovo District, Lapino 143081

blinov2010@googlemail.comИнститут Превентивной и Социальной Медицины; Клинический госпиталь «Лапино» группы компаний «Мать и Дитя»РоссияInstitute for Preventive and Social Medicine; Lapino Clinical Hospital, Medical Group “Mother and Child”Russian Federation202227072022142101182Copyright © Blinov D.V., 20222022Блинов Д.В.Blinov D.V.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.epilepsia.su/jour/article/view/792

Until recently, no classification of epileptic syndromes officially approved by the International League Against Epilepsy (ILAE) was available. In 2022, owing to many year-persistent efforts made by experts and the public community, the studies providing the definition and classification of epileptic syndromes were published. ILAE has approved the following definition of the epileptic syndrome: “a characteristic cluster of clinical and EEG features, often supported by specific etiological findings (structural, genetic, metabolic, immune, and infectious)”. The classification of epileptic syndromes is proposed according to the age principle: onset in neonates and infants, onset in childhood, onset at a variable age. Separately, the syndromes of idiopathic generalized epilepsy were presented. Clinical data for each epileptic syndrome are presented in a single pattern: epidemiology, clinical context, natural history, type(s) of seizures, electroencephalography, neuroimaging findings, genetic findings, other laboratory findings (when informative), differential diagnosis. The criteria for diagnosis, including mandatory criteria, warning signs and exclusion criteria, are given. This classification should be a starting point for further improvement in the organizing work of practitioners who deal with epilepsy.

До недавнего времени не было официально утвержденной Международной Противоэпилептической Лигой (англ. International League Against Epilepsy, ILAE) классификации эпилептических синдромов. В 2022 г. в результате многолетних упорных усилий экспертов и общественности вышли в свет работы, представляющие определение и классификацию эпилептических синдромов. ILAE утвердила следующее определение эпилептического синдрома: «характерный набор клинических и электроэнцефалографических признаков, часто обусловленных специфическими этиологическими факторами (структурными, генетическими, метаболическими, иммунными и инфекционными)». Классификация эпилептических синдромов выполнена по возрастному принципу: с началом в неонатальном периоде и младенчестве, с началом в детском возрасте, с началом в разном возрасте. Отдельно были выделены синдромы идиопатической генерализованной эпилепсии. Клинические данные по каждому эпилептическому синдрому приведены в едином шаблоне: эпидемиология, клиническая картина, анамнез заболевания, тип(ы) приступов, данные электроэнцефалографии, результаты нейровизуализации, данные генетических исследований, результаты других лабораторных исследований (когда они информативны), дифференциальный диагноз. Приводятся критерии постановки диагноза, включающие обязательные критерии, настораживающие признаки и критерии исключения. Эта классификация должна стать отправной точкой для дальнейшего улучшения организации работы практикующих специалистов, которые занимаются проблемой эпилепсии.

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The authors declare that there are no conflicts of interest present.