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RÜLFS CRAMP AND OTHER PAROXYSMAL DYSKINESIA

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Abstract

Paroxysmal dyskinesia comprise a significant and fascinating part of movement disorders, which represent a diagnostic challenge for neurologists working on the borderlands of psychiatry and epilepsy. The current classification based on the relation of attacks to a movement is supported by the response to treatment and genetic difference. We reviewed clinical characteristics and the main advances in genetics of these unique, usually hereditary diseases. Clinical diagnosis remains the key to the treatment choice. Psychogenic causes are common in sporadic cases, but paroxysmal dyskinesia secondary to systemic or primary neurological disorders should not be missed and warrant careful investigation.

About the Authors

M. V. Selikhova
Pirogov Russian National Research Medical University, Moscow; Institute of Neurology in London
Russian Federation

Selihova Marianna Valerievna – Ph.D. Senior Researcher, Consultant Neurologist. 

Address: ul. Ostrovityanova, d. 1, Moscow, Russia, 117997



Z. Z. Zalyalova
Republican Clinical Diagnostic Center of extrapyramidal pathology and Botulinum, Kazan
Russian Federation

Zalyalova Zuleikha Zalyalova – MD, professor of neurology and rehabilitation at Kazan State Medical University, head of the Republican Clinical Diagnostic Center extrapyramidal pathology and Botulinum.

Address: Str. Butlerova 49, Kazan, Republic of Tatarstan, Russia, 420012



N. I. Bogdanova
Republican Clinical Diagnostic Center of extrapyramidal pathology and Botulinum, Kazan
Russian Federation

Bagdanova Nailya Iskanderovna – Post-graduate student of the department of neurology and rehabilitation a tKazan State Medical University.

Address: Str. Butlerova 49, Kazan, Republic of Tatarstan, Russia, 420012. 



G. G. Avakyan
Pirogov Russian National Research Medical University, Moscow
Russian Federation

Avakyan George Gagikovich – MD, PhD, Department of Neurology, Neurosurgery and Medical Genetics. 

Address: ul. Ostrovityanova, d. 1, Moscow, Russia, 117997.



G. Houlden
Institute of Neurology, London
United Kingdom

Houlden Henry – Professor of Neurology, Head. Laboratory of Neurogenetics. Address:Queen Square, WCN 3BG.



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For citation:


Selikhova M.V., Zalyalova Z.Z., Bogdanova N.I., Avakyan G.G., Houlden G. RÜLFS CRAMP AND OTHER PAROXYSMAL DYSKINESIA. Epilepsy and paroxysmal conditions. 2015;7(3):40-45. (In Russ.)

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ISSN 2077-8333 (Print)
ISSN 2311-4088 (Online)