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New-Onset Refractory Status Epilepticus (NORSE): literature review and clinical case description

https://doi.org/10.17749/2077-8333/epi.par.con.2020.034

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Abstract

Here we provide a literature-based definition as well as etiological factors, clinical picture, prognosis, diagnostic algorithm, and treatment for the New-Onset Refractory Status Epilepticus (NORSE syndrome). In addition, we also present our personal experience by describing a female patient with refractory focal epilepsy associated with the cryptogenic new-onset refractory status epilepticus.

About the Authors

S. G. Burd
Federal Center for Brain and Neurotechnologies of the Federal Medical and Biological Agency; Pirogov Russian National Research Medical University
Russian Federation

Sergey G. Burd- MD, Dr Sci Med, Professor at the Department of Neurology, Neurosurgery and Medical Genetics, Faculty of Pediatrics, Pirogov RNRMU, Ministry of Health of the Russian Federation; Head of the Department of Paroxysmal Diseases, Federal Center for Brain and Neurotechnologies FMBA.

1-10 Ostrovityanova Str., Moscow 117997; 1 Ostrovityanova Str., Moscow 117997



M. B. Mironov
Federal Center for Brain and Neurotechnologies of the Federal Medical and Biological Agency
Russian Federation

Mikhail B. Mironov - MD, PhD, Leading Researcher, Department of Epilepsy and Paroxysmal Conditions, Scopus ID: 632779; RSCI SPIN-code: 1144-7120.

1-10 Ostrovityanova Str., Moscow 117997



E. R. Moizykevich
Federal Center for Brain and Neurotechnologies of the Federal Medical and Biological Agency
Russian Federation

 

Elena R. Moizykevich - Junior Researcher, Department of Paroxysmal Diseases, Department of Epilepsy and Paroxysmal Conditions.

1-10 Ostrovityanova Str., Moscow 117997



Yu. V. Rubleva
Federal Center for Brain and Neurotechnologies of the Federal Medical and Biological Agency
Russian Federation

Yulia V. Rubleva - MD, PhD, Senior Researcher for Epilepsy and Paroxysmal Conditions, Federal Center for Brain and Neurotechnologies FMBA; Head of the Department of Neurology No. 1, Federal Center for Brain and Neurotechnologies of the FMBA.

1-10 Ostrovityanova Str., Moscow 117997


M. A. Bogomazova
Federal Center for Brain and Neurotechnologies of the Federal Medical and Biological Agency
Russian Federation

 

Maria A. Bogomazova - neurologist of the Department of Neurology No. 1.

1-10 Ostrovityanova Str., Moscow 117997



А. V. Yurchenko
Federal Center for Brain and Neurotechnologies of the Federal Medical and Biological Agency
Russian Federation

 

Anna V. Yurchenko - neurologist of the Department of Neurology No. 1.

1-10 Ostrovityanova Str., Moscow 117997



T. M. Krasilshchikova
Pirogov Russian National Research Medical University
Russian Federation

 

Tatyana M. Krasilshchikova - MD, Assistant, Chair of Neurology, Neurosurgery and Medical Genetics, Faculty of Pediatrics.

1 Ostrovityanova Str., Moscow 117997



A. Yu. Suvorov
Federal Center for Brain and Neurotechnologies of the Federal Medical and Biological Agency; Pirogov Russian National Research Medical University
Russian Federation

Andrey Yu. Suvorov - MD, PhD, Scientific Secretary, Federal Center for Brain and Neurotechnologies of the Federal Medical and Biological Agency; Associate Professor of the Department of Medical Rehabilitation, Pirogov RNRMU.

1-10 Ostrovityanova Str., Moscow 117997; 1 Ostrovityanova Str., Moscow 117997



A. V. Lebedeva
Pirogov Russian National Research Medical University
Russian Federation

Anna V. Lebedeva - MD, Dr Sci Med, Professor at the Department of Neurology, Neurosurgery and Medical Genetics, Faculty of Pediatrics.

1 Ostrovityanova Str., Moscow 117997



R. T. Tairova
Federal Center for Brain and Neurotechnologies of the Federal Medical and Biological Agency
Russian Federation

Raisa T. Tairova - MD, PhD, Deputy Director for Medical Work, Chief Physician of the Federal State Budgetary Institution.

1-10 Ostrovityanova Str., Moscow 117997



References

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Review

For citations:


Burd S.G., Mironov M.B., Moizykevich E.R., Rubleva Yu.V., Bogomazova M.A., Yurchenko А.V., Krasilshchikova T.M., Suvorov A.Yu., Lebedeva A.V., Tairova R.T. New-Onset Refractory Status Epilepticus (NORSE): literature review and clinical case description. Epilepsy and paroxysmal conditions. 2020;12(3):169-176. (In Russ.) https://doi.org/10.17749/2077-8333/epi.par.con.2020.034

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ISSN 2077-8333 (Print)
ISSN 2311-4088 (Online)