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FEJERMAN SYNDROME (BENIGN NONEPILEPTIC MYOCLONUS OF INFANCY)

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Abstract

Abstract: Fejerman syndrome (benign nonepileptic myoclonus of infancy) is a rare nonepileptic paroxysmal disorder, characterized by typical presentation of short head nodding or shuddering in otherwise healthy infant without focal signs or psychomotor retardation and not associated with epileptiform abnormalities on EEG. Onset of this disorder occurs at first year of life (predominantly 6 months). Prognosis is benign with spontaneous disappearing of paroxysmal episodes by age of 2-3 years. This syndrome is poorly described in Russian literature. We present the description of our own clinical cases.

About the Authors

M. B. Mironov
St. Luka’s Institute of Child Neurology and Epilepsy, Moscow
Russian Federation


V. Iu. Nogovitsyn
Morozovskaya Children’s Hospital, Moscow
Russian Federation


M. O. Abramov
St. Luka’s Institute of Child Neurology and Epilepsy, Moscow
Russian Federation


E. A. Dobrovskaya
Morozovskaya Children’s Hospital, Moscow
Russian Federation


N. E. Kvaskova
St. Luka’s Institute of Child Neurology and Epilepsy, Moscow
Russian Federation


K. Yu. Mukhin
St. Luka’s Institute of Child Neurology and Epilepsy, Moscow
Russian Federation


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For citation:


Mironov M.B., Nogovitsyn V.I., Abramov M.O., Dobrovskaya E.A., Kvaskova N.E., Mukhin K.Y. FEJERMAN SYNDROME (BENIGN NONEPILEPTIC MYOCLONUS OF INFANCY). Epilepsy and paroxysmal conditions. 2013;5(2):42-46. (In Russ.)

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ISSN 2077-8333 (Print)
ISSN 2311-4088 (Online)